Malignant ectomesenchymoma in the wrist of a child: Case report and review of the literature

Orit Oppenheimer, Edward Athanasian, Paul Meyers, Cristina R. Antonescu, Richard Gorlick

Research output: Contribution to journalReview article

10 Scopus citations

Abstract

Malignant ectomesenchymomas, rare and potentially aggressive tumors, occur in children and exhibit mesenchymal and neuroectodermal components. This report describes the first patient diagnosed with a malignant ectomesenchymoma of the hand. The patient was a 17-month-old male who developed a hypothenar mass on his left hand that was surgically excised. Microscopic evaluation revealed ganglioneuroblastic, rhabdomyosarcomatous, and chondrosarcomatous elements. Following excisional biopsy he was treated with cyclophosphamide, doxorubicin, vincristine, ifosfamide, and etoposide. After 3 courses of chemotherapy the patient had a wide reexcision with no residual tumor. The patient is 4 years from diagnosis, without evidence of disease.

Original languageEnglish (US)
Pages (from-to)113-116
Number of pages4
JournalInternational Journal of Surgical Pathology
Volume13
Issue number1
DOIs
StatePublished - Jan 2005

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Keywords

  • Chemotherapy
  • Malignant ectomesenchymoma
  • Pediatric tumors

ASJC Scopus subject areas

  • Anatomy
  • Surgery
  • Pathology and Forensic Medicine

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