Abstract
Langerhans cell histiocytosis (LCH) is a disorder associated with proliferation of Langerhans cells in various organs. LCH secondary to multisystem involvement can present in a variety of ways. Because of its infiltrative nature, LCH can involve the skin, lymph nodes, the lung or the liver. Jaundice in LCH is a manifestation of liver disease; biliary dilatation secondary to lithiasis or may be due to coexistent Niemann-Pick disease. However, a case of cholestasis has been very rarely described. Cholestasis may result from lymph nodes obstructing the porta hepatis. In this report, we describe a case of type II histiocytosis X with obstructive cholestasis and pulmonary involvement in the form of cysts without significant lymphadenopathy at the porta.
Original language | English (US) |
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Pages (from-to) | SD03-SD05 |
Journal | Journal of Clinical and Diagnostic Research |
Volume | 9 |
Issue number | 2 |
DOIs | |
State | Published - 2015 |
Keywords
- Cholestasis
- Lymphadenopathy
- Porta hepatis
ASJC Scopus subject areas
- Clinical Biochemistry