TRANSPLANTATION HEPATIQUE ET RENALE DANS LE TRAITEMENT DE L'HYPEROXALURIE DE TYPE I

P. Jouvet; P. Hubert; D. Jan; P. Niaudet; A. Beringer; C. Narcy; M. Daudon; M. Broyer; Y. Revillon

TRANSPLANTATION HEPATIQUE ET RENALE DANS LE TRAITEMENT DE L'HYPEROXALURIE DE TYPE I

Translated title of the contribution: Combined hepatic and renal transplantation for primary hyperoxaluria type I

P. Jouvet, P. Hubert, D. Jan, P. Niaudet, A. Beringer, C. Narcy, M. Daudon, M. Broyer, Y. Revillon

Research output: Contribution to journal › Article › peer-review

2 Scopus citations

Abstract

Hyperoxaluria type I (HPI) is a metabolic disorder secondary to liver alanine glyoxylate aminotransferase deficiency. Renal failure occurs due to the excessive production and precipitation of oxalate in the kidney. Combined liver-renal transplantation is the correct treatment for this condition when end-stage renal failure occurs as with renal transplantation alone the risk of recurrence of the same pathology in the transplanted kidney would be high. We report the case of a 4 year-old child with HPI suffering from terminal renal failure in whom a hepato-renal transplantation was performed: six months later, creatinine clearance was 62 ml/min/1.73 m² and liver function tests were normal.

Translated title of the contribution	Combined hepatic and renal transplantation for primary hyperoxaluria type I
Original language	French
Pages (from-to)	637-639
Number of pages	3
Journal	Archives Francaises de Pediatrie
Volume	48
Issue number	9
State	Published - Jan 1 1991
Externally published	Yes

Keywords

child
hyperoxaluria
kidney failure, chronic
liver
metabolism, inborn errors
transplantation

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health

Cite this

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abstract = "Hyperoxaluria type I (HPI) is a metabolic disorder secondary to liver alanine glyoxylate aminotransferase deficiency. Renal failure occurs due to the excessive production and precipitation of oxalate in the kidney. Combined liver-renal transplantation is the correct treatment for this condition when end-stage renal failure occurs as with renal transplantation alone the risk of recurrence of the same pathology in the transplanted kidney would be high. We report the case of a 4 year-old child with HPI suffering from terminal renal failure in whom a hepato-renal transplantation was performed: six months later, creatinine clearance was 62 ml/min/1.73 m2 and liver function tests were normal.",

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AU - Jouvet, P.

AU - Hubert, P.

AU - Jan, D.

AU - Niaudet, P.

AU - Beringer, A.

AU - Narcy, C.

AU - Daudon, M.

AU - Broyer, M.

AU - Revillon, Y.

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AB - Hyperoxaluria type I (HPI) is a metabolic disorder secondary to liver alanine glyoxylate aminotransferase deficiency. Renal failure occurs due to the excessive production and precipitation of oxalate in the kidney. Combined liver-renal transplantation is the correct treatment for this condition when end-stage renal failure occurs as with renal transplantation alone the risk of recurrence of the same pathology in the transplanted kidney would be high. We report the case of a 4 year-old child with HPI suffering from terminal renal failure in whom a hepato-renal transplantation was performed: six months later, creatinine clearance was 62 ml/min/1.73 m2 and liver function tests were normal.

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KW - kidney failure, chronic

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KW - metabolism, inborn errors

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TRANSPLANTATION HEPATIQUE ET RENALE DANS LE TRAITEMENT DE L'HYPEROXALURIE DE TYPE I

Abstract

Keywords

ASJC Scopus subject areas

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