TRANSPLANTATION HEPATIQUE ET RENALE DANS LE TRAITEMENT DE L'HYPEROXALURIE DE TYPE I

Translated title of the contribution: Combined hepatic and renal transplantation for primary hyperoxaluria type I

P. Jouvet, P. Hubert, D. Jan, P. Niaudet, A. Beringer, C. Narcy, M. Daudon, M. Broyer, Y. Revillon

Research output: Contribution to journalArticle

2 Scopus citations

Abstract

Hyperoxaluria type I (HPI) is a metabolic disorder secondary to liver alanine glyoxylate aminotransferase deficiency. Renal failure occurs due to the excessive production and precipitation of oxalate in the kidney. Combined liver-renal transplantation is the correct treatment for this condition when end-stage renal failure occurs as with renal transplantation alone the risk of recurrence of the same pathology in the transplanted kidney would be high. We report the case of a 4 year-old child with HPI suffering from terminal renal failure in whom a hepato-renal transplantation was performed: six months later, creatinine clearance was 62 ml/min/1.73 m2 and liver function tests were normal.

Translated title of the contributionCombined hepatic and renal transplantation for primary hyperoxaluria type I
Original languageFrench
Pages (from-to)637-639
Number of pages3
JournalArchives Francaises de Pediatrie
Volume48
Issue number9
StatePublished - Jan 1 1991
Externally publishedYes

Keywords

  • child
  • hyperoxaluria
  • kidney failure, chronic
  • liver
  • metabolism, inborn errors
  • transplantation

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

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    Jouvet, P., Hubert, P., Jan, D., Niaudet, P., Beringer, A., Narcy, C., Daudon, M., Broyer, M., & Revillon, Y. (1991). TRANSPLANTATION HEPATIQUE ET RENALE DANS LE TRAITEMENT DE L'HYPEROXALURIE DE TYPE I. Archives Francaises de Pediatrie, 48(9), 637-639.