Anesthetic Management of a Pediatric Patient With Pelizaeus-Merzbacher Syndrome

A Case Report

Roshan S. Patel, Madelyn Kahana

Research output: Contribution to journalArticle

Abstract

A 3-year-old pediatric patient with previously diagnosed Pelizaeus-Merzbacher syndrome presented for outpatient dental restoration. Given the infrequency of this demyelinating disorder, an anesthetic plan was tailored to address the patient's hypotonia and aspiration risk, as well as minimize potential complications including seizures, hemodynamic instability, and postoperative respiratory support. Multimodal analgesia, along with an appropriate ventilation strategy and normothermia, allowed the patient to successfully undergo a general anesthetic and be safely discharged home the same day.

Original languageEnglish (US)
Pages (from-to)351-352
Number of pages2
JournalA&A practice
Volume11
Issue number12
DOIs
StatePublished - Dec 15 2018

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Anesthetics
Pediatrics
General Anesthetics
Muscle Hypotonia
Demyelinating Diseases
Analgesia
Ventilation
Tooth
Seizures
Outpatients
Hemodynamics

Cite this

Anesthetic Management of a Pediatric Patient With Pelizaeus-Merzbacher Syndrome : A Case Report. / Patel, Roshan S.; Kahana, Madelyn.

In: A&A practice, Vol. 11, No. 12, 15.12.2018, p. 351-352.

Research output: Contribution to journalArticle

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