TY - JOUR
T1 - UNUSUAL COMBINED IMMUNODEFICIENCY SYNDROME EXHIBITING KAPPA‐IGD PARAPROTEINEMIA, RESIDUAL GUT‐IMMUNITY AND GRAFT‐VERSUS‐HOST REACTION AFTER PLASMA INFUSION
AU - RUBINSTEIN, A.
AU - RÁADL, J.
AU - COTTIER, H.
AU - ROSSI, E.
AU - GUGLER, E.
PY - 1973/7
Y1 - 1973/7
N2 - A 12‐year‐old suffering from a lymphopenic severe CID with an unusual protracted clinical course is presented. His gut‐associated lympho‐epithelial system was apparently normal, in contrast to the IgA deficiency in other external fluids. In addition, an elevated kappa‐IgD was detected in his serum. Fresh plasma infusions from unrelated donors induced an accidental engraftment with a moderate non‐fatal GvHR.
AB - A 12‐year‐old suffering from a lymphopenic severe CID with an unusual protracted clinical course is presented. His gut‐associated lympho‐epithelial system was apparently normal, in contrast to the IgA deficiency in other external fluids. In addition, an elevated kappa‐IgD was detected in his serum. Fresh plasma infusions from unrelated donors induced an accidental engraftment with a moderate non‐fatal GvHR.
KW - Combined immune deficiency
KW - dinitro‐chlorobenzene
KW - graft‐versus‐host reaction
KW - mixed lymphocyte culture
KW - phytohemagglutinin
KW - purified protein derivative
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U2 - 10.1111/j.1651-2227.1973.tb08121.x
DO - 10.1111/j.1651-2227.1973.tb08121.x
M3 - Article
C2 - 4125769
AN - SCOPUS:0015849936
SN - 0803-5253
VL - 62
SP - 365
EP - 372
JO - Acta Paediatrica Scandinavica
JF - Acta Paediatrica Scandinavica
IS - 4
ER -