UNUSUAL COMBINED IMMUNODEFICIENCY SYNDROME EXHIBITING KAPPA‐IGD PARAPROTEINEMIA, RESIDUAL GUT‐IMMUNITY AND GRAFT‐VERSUS‐HOST REACTION AFTER PLASMA INFUSION

A. RUBINSTEIN, J. RÁADL, H. COTTIER, E. ROSSI, E. GUGLER

Research output: Contribution to journalArticle

44 Scopus citations

Abstract

A 12‐year‐old suffering from a lymphopenic severe CID with an unusual protracted clinical course is presented. His gut‐associated lympho‐epithelial system was apparently normal, in contrast to the IgA deficiency in other external fluids. In addition, an elevated kappa‐IgD was detected in his serum. Fresh plasma infusions from unrelated donors induced an accidental engraftment with a moderate non‐fatal GvHR.

Original languageEnglish (US)
Pages (from-to)365-372
Number of pages8
JournalActa Pædiatrica
Volume62
Issue number4
DOIs
StatePublished - Jul 1973
Externally publishedYes

Keywords

  • Combined immune deficiency
  • dinitro‐chlorobenzene
  • graft‐versus‐host reaction
  • mixed lymphocyte culture
  • phytohemagglutinin
  • purified protein derivative

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

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