UNUSUAL COMBINED IMMUNODEFICIENCY SYNDROME EXHIBITING KAPPA‐IGD PARAPROTEINEMIA, RESIDUAL GUT‐IMMUNITY AND GRAFT‐VERSUS‐HOST REACTION AFTER PLASMA INFUSION

A. RUBINSTEIN; J. RÁADL; H. COTTIER; E. ROSSI; E. GUGLER

doi:10.1111/j.1651-2227.1973.tb08121.x

UNUSUAL COMBINED IMMUNODEFICIENCY SYNDROME EXHIBITING KAPPA‐IGD PARAPROTEINEMIA, RESIDUAL GUT‐IMMUNITY AND GRAFT‐VERSUS‐HOST REACTION AFTER PLASMA INFUSION

A. RUBINSTEIN, J. RÁADL, H. COTTIER, E. ROSSI, E. GUGLER

Research output: Contribution to journal › Article › peer-review

49 Scopus citations

Abstract

A 12‐year‐old suffering from a lymphopenic severe CID with an unusual protracted clinical course is presented. His gut‐associated lympho‐epithelial system was apparently normal, in contrast to the IgA deficiency in other external fluids. In addition, an elevated kappa‐IgD was detected in his serum. Fresh plasma infusions from unrelated donors induced an accidental engraftment with a moderate non‐fatal GvHR.

Original language	English (US)
Pages (from-to)	365-372
Number of pages	8
Journal	Acta Pædiatrica
Volume	62
Issue number	4
DOIs	https://doi.org/10.1111/j.1651-2227.1973.tb08121.x
State	Published - Jul 1973
Externally published	Yes

Keywords

Combined immune deficiency
dinitro‐chlorobenzene
graft‐versus‐host reaction
mixed lymphocyte culture
phytohemagglutinin
purified protein derivative

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health

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10.1111/j.1651-2227.1973.tb08121.x

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title = "UNUSUAL COMBINED IMMUNODEFICIENCY SYNDROME EXHIBITING KAPPA‐IGD PARAPROTEINEMIA, RESIDUAL GUT‐IMMUNITY AND GRAFT‐VERSUS‐HOST REACTION AFTER PLASMA INFUSION",

abstract = "A 12‐year‐old suffering from a lymphopenic severe CID with an unusual protracted clinical course is presented. His gut‐associated lympho‐epithelial system was apparently normal, in contrast to the IgA deficiency in other external fluids. In addition, an elevated kappa‐IgD was detected in his serum. Fresh plasma infusions from unrelated donors induced an accidental engraftment with a moderate non‐fatal GvHR.",

keywords = "Combined immune deficiency, dinitro‐chlorobenzene, graft‐versus‐host reaction, mixed lymphocyte culture, phytohemagglutinin, purified protein derivative",

author = "A. RUBINSTEIN and J. R{\'A}ADL and H. COTTIER and E. ROSSI and E. GUGLER",

year = "1973",

month = jul,

doi = "10.1111/j.1651-2227.1973.tb08121.x",

language = "English (US)",

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TY - JOUR

T1 - UNUSUAL COMBINED IMMUNODEFICIENCY SYNDROME EXHIBITING KAPPA‐IGD PARAPROTEINEMIA, RESIDUAL GUT‐IMMUNITY AND GRAFT‐VERSUS‐HOST REACTION AFTER PLASMA INFUSION

AU - RUBINSTEIN, A.

AU - RÁADL, J.

AU - COTTIER, H.

AU - ROSSI, E.

AU - GUGLER, E.

PY - 1973/7

Y1 - 1973/7

N2 - A 12‐year‐old suffering from a lymphopenic severe CID with an unusual protracted clinical course is presented. His gut‐associated lympho‐epithelial system was apparently normal, in contrast to the IgA deficiency in other external fluids. In addition, an elevated kappa‐IgD was detected in his serum. Fresh plasma infusions from unrelated donors induced an accidental engraftment with a moderate non‐fatal GvHR.

AB - A 12‐year‐old suffering from a lymphopenic severe CID with an unusual protracted clinical course is presented. His gut‐associated lympho‐epithelial system was apparently normal, in contrast to the IgA deficiency in other external fluids. In addition, an elevated kappa‐IgD was detected in his serum. Fresh plasma infusions from unrelated donors induced an accidental engraftment with a moderate non‐fatal GvHR.

KW - Combined immune deficiency

KW - dinitro‐chlorobenzene

KW - graft‐versus‐host reaction

KW - mixed lymphocyte culture

KW - phytohemagglutinin

KW - purified protein derivative

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DO - 10.1111/j.1651-2227.1973.tb08121.x

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AN - SCOPUS:0015849936

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UNUSUAL COMBINED IMMUNODEFICIENCY SYNDROME EXHIBITING KAPPA‐IGD PARAPROTEINEMIA, RESIDUAL GUT‐IMMUNITY AND GRAFT‐VERSUS‐HOST REACTION AFTER PLASMA INFUSION

Abstract

Keywords

ASJC Scopus subject areas

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