Systemic necrotizing vasculitis associated with childhood sarcoidosis

Terry Kwong, Elsa Valderrama, Carole Paley, Norman Ilowite

Research output: Contribution to journalArticlepeer-review

33 Scopus citations


Childhood sarcoidosis is a rare disorder with protean manifestations. The case of a child with prolonged fever, hepatosplenomegaly, pancytopenia, and systemic necrotizing vasculitis manifesting as fever, rash and skin infarctions, digital pregangrene, and foot drop is reported. This is the first case of systemic necrotizing vasculitis reported in sarcoidosis. The fulminant course of the disease required treatment with intravenous pulsed cyclophosphamide and high doses of corticosteroids. The spectrum of vasculitis in childhood and adult sarcoidosis is reviewed.

Original languageEnglish (US)
Pages (from-to)388-395
Number of pages8
JournalSeminars in Arthritis and Rheumatism
Issue number6
StatePublished - Jun 1994


  • Sarcoidosis
  • granulomatous disease
  • vasculitis

ASJC Scopus subject areas

  • Rheumatology
  • Anesthesiology and Pain Medicine


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