Respiratory Muscle Dysfunction in Hereditary Motor Sensory Neuropathy, Type I

Peter Q. Eichacker, Alfred Spiro, Michael Sherman, Eliot Lazar, Joseph Reichel, Fran Dodick

Research output: Contribution to journalArticle

23 Citations (Scopus)

Abstract

Pulmonary function tests were performed on ten patients who were shown to have hereditary motor sensory neuropathy, type I. Mean values for spirometry, static lung volumes, and diffusion capacity were all greater than 80% of the predicted normal values for the group. In contrast, both inspiratory and expiratory muscle testing showed substantial reductions in function for the group. These abnormalities have not previously been reported, and they may be important in the management of these patients and in patients with other neuromuscular diseases.

Original languageEnglish (US)
Pages (from-to)1739-1740
Number of pages2
JournalArchives of Internal Medicine
Volume148
Issue number8
DOIs
StatePublished - 1988

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Charcot-Marie-Tooth Disease
Respiratory Muscles
Neuromuscular Diseases
Spirometry
Respiratory Function Tests
Reference Values
Muscles
Lung

ASJC Scopus subject areas

  • Internal Medicine

Cite this

Eichacker, P. Q., Spiro, A., Sherman, M., Lazar, E., Reichel, J., & Dodick, F. (1988). Respiratory Muscle Dysfunction in Hereditary Motor Sensory Neuropathy, Type I. Archives of Internal Medicine, 148(8), 1739-1740. https://doi.org/10.1001/archinte.1988.00380080041013

Respiratory Muscle Dysfunction in Hereditary Motor Sensory Neuropathy, Type I. / Eichacker, Peter Q.; Spiro, Alfred; Sherman, Michael; Lazar, Eliot; Reichel, Joseph; Dodick, Fran.

In: Archives of Internal Medicine, Vol. 148, No. 8, 1988, p. 1739-1740.

Research output: Contribution to journalArticle

Eichacker, PQ, Spiro, A, Sherman, M, Lazar, E, Reichel, J & Dodick, F 1988, 'Respiratory Muscle Dysfunction in Hereditary Motor Sensory Neuropathy, Type I', Archives of Internal Medicine, vol. 148, no. 8, pp. 1739-1740. https://doi.org/10.1001/archinte.1988.00380080041013
Eichacker, Peter Q. ; Spiro, Alfred ; Sherman, Michael ; Lazar, Eliot ; Reichel, Joseph ; Dodick, Fran. / Respiratory Muscle Dysfunction in Hereditary Motor Sensory Neuropathy, Type I. In: Archives of Internal Medicine. 1988 ; Vol. 148, No. 8. pp. 1739-1740.
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