TY - JOUR
T1 - Respiratory Muscle Dysfunction in Hereditary Motor Sensory Neuropathy, Type I
AU - Eichacker, Peter Q.
AU - Spiro, Alfred
AU - Sherman, Michael
AU - Lazar, Eliot
AU - Reichel, Joseph
AU - Dodick, Fran
PY - 1988/8
Y1 - 1988/8
N2 - Pulmonary function tests were performed on ten patients who were shown to have hereditary motor sensory neuropathy, type I. Mean values for spirometry, static lung volumes, and diffusion capacity were all greater than 80% of the predicted normal values for the group. In contrast, both inspiratory and expiratory muscle testing showed substantial reductions in function for the group. These abnormalities have not previously been reported, and they may be important in the management of these patients and in patients with other neuromuscular diseases.
AB - Pulmonary function tests were performed on ten patients who were shown to have hereditary motor sensory neuropathy, type I. Mean values for spirometry, static lung volumes, and diffusion capacity were all greater than 80% of the predicted normal values for the group. In contrast, both inspiratory and expiratory muscle testing showed substantial reductions in function for the group. These abnormalities have not previously been reported, and they may be important in the management of these patients and in patients with other neuromuscular diseases.
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U2 - 10.1001/archinte.1988.00380080041013
DO - 10.1001/archinte.1988.00380080041013
M3 - Article
C2 - 3401096
AN - SCOPUS:0023688950
SN - 2168-6106
VL - 148
SP - 1739
EP - 1740
JO - Archives of internal medicine (Chicago, Ill. : 1908)
JF - Archives of internal medicine (Chicago, Ill. : 1908)
IS - 8
ER -