MRI assessment of bronchial compression in absent pulmonary valve syndrome and review of the syndrome

Benjamin H. Taragin, Walter E. Berdon, Beth Printz

Research output: Contribution to journalReview article

14 Scopus citations

Abstract

Absent pulmonary valve syndrome (APVS) is a rare cardiac malformation with massive pulmonary insufficiency that presents with short-term and long-term respiratory problems secondary to severe bronchial compression from enlarged central and hilar pulmonary arteries. Association with chromosome 22.Q11 deletions and DiGeorge syndrome is common. This historical review illustrates the airway disease with emphasis on assessment of the bronchial compression in patients with persistent respiratory difficulties post-valvular repair. Cases that had MRI for cardiac assessment are used to illustrate the pattern of airway disease.

Original languageEnglish (US)
Pages (from-to)71-75
Number of pages5
JournalPediatric radiology
Volume36
Issue number1
DOIs
StatePublished - Jan 2006

Keywords

  • Absent pulmonary valve syndrome
  • Airway abnormalities
  • MRI

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Radiology Nuclear Medicine and imaging

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