MRI assessment of bronchial compression in absent pulmonary valve syndrome and review of the syndrome

Benjamin H. Taragin, Walter E. Berdon, Beth Printz

Research output: Contribution to journalArticle

13 Citations (Scopus)

Abstract

Absent pulmonary valve syndrome (APVS) is a rare cardiac malformation with massive pulmonary insufficiency that presents with short-term and long-term respiratory problems secondary to severe bronchial compression from enlarged central and hilar pulmonary arteries. Association with chromosome 22.Q11 deletions and DiGeorge syndrome is common. This historical review illustrates the airway disease with emphasis on assessment of the bronchial compression in patients with persistent respiratory difficulties post-valvular repair. Cases that had MRI for cardiac assessment are used to illustrate the pattern of airway disease.

Original languageEnglish (US)
Pages (from-to)71-75
Number of pages5
JournalPediatric Radiology
Volume36
Issue number1
DOIs
StatePublished - Jan 2006
Externally publishedYes

Fingerprint

Pulmonary Valve
DiGeorge Syndrome
Chromosomes, Human, Pair 22
Pulmonary Artery
Lung

Keywords

  • Absent pulmonary valve syndrome
  • Airway abnormalities
  • MRI

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging
  • Pediatrics, Perinatology, and Child Health
  • Radiological and Ultrasound Technology

Cite this

MRI assessment of bronchial compression in absent pulmonary valve syndrome and review of the syndrome. / Taragin, Benjamin H.; Berdon, Walter E.; Printz, Beth.

In: Pediatric Radiology, Vol. 36, No. 1, 01.2006, p. 71-75.

Research output: Contribution to journalArticle

Taragin, Benjamin H. ; Berdon, Walter E. ; Printz, Beth. / MRI assessment of bronchial compression in absent pulmonary valve syndrome and review of the syndrome. In: Pediatric Radiology. 2006 ; Vol. 36, No. 1. pp. 71-75.
@article{195ebe05230240e3918dc73dbaae8534,
title = "MRI assessment of bronchial compression in absent pulmonary valve syndrome and review of the syndrome",
abstract = "Absent pulmonary valve syndrome (APVS) is a rare cardiac malformation with massive pulmonary insufficiency that presents with short-term and long-term respiratory problems secondary to severe bronchial compression from enlarged central and hilar pulmonary arteries. Association with chromosome 22.Q11 deletions and DiGeorge syndrome is common. This historical review illustrates the airway disease with emphasis on assessment of the bronchial compression in patients with persistent respiratory difficulties post-valvular repair. Cases that had MRI for cardiac assessment are used to illustrate the pattern of airway disease.",
keywords = "Absent pulmonary valve syndrome, Airway abnormalities, MRI",
author = "Taragin, {Benjamin H.} and Berdon, {Walter E.} and Beth Printz",
year = "2006",
month = "1",
doi = "10.1007/s00247-005-0018-9",
language = "English (US)",
volume = "36",
pages = "71--75",
journal = "Pediatric Radiology",
issn = "0301-0449",
publisher = "Springer Verlag",
number = "1",

}

TY - JOUR

T1 - MRI assessment of bronchial compression in absent pulmonary valve syndrome and review of the syndrome

AU - Taragin, Benjamin H.

AU - Berdon, Walter E.

AU - Printz, Beth

PY - 2006/1

Y1 - 2006/1

N2 - Absent pulmonary valve syndrome (APVS) is a rare cardiac malformation with massive pulmonary insufficiency that presents with short-term and long-term respiratory problems secondary to severe bronchial compression from enlarged central and hilar pulmonary arteries. Association with chromosome 22.Q11 deletions and DiGeorge syndrome is common. This historical review illustrates the airway disease with emphasis on assessment of the bronchial compression in patients with persistent respiratory difficulties post-valvular repair. Cases that had MRI for cardiac assessment are used to illustrate the pattern of airway disease.

AB - Absent pulmonary valve syndrome (APVS) is a rare cardiac malformation with massive pulmonary insufficiency that presents with short-term and long-term respiratory problems secondary to severe bronchial compression from enlarged central and hilar pulmonary arteries. Association with chromosome 22.Q11 deletions and DiGeorge syndrome is common. This historical review illustrates the airway disease with emphasis on assessment of the bronchial compression in patients with persistent respiratory difficulties post-valvular repair. Cases that had MRI for cardiac assessment are used to illustrate the pattern of airway disease.

KW - Absent pulmonary valve syndrome

KW - Airway abnormalities

KW - MRI

UR - http://www.scopus.com/inward/record.url?scp=33244469496&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=33244469496&partnerID=8YFLogxK

U2 - 10.1007/s00247-005-0018-9

DO - 10.1007/s00247-005-0018-9

M3 - Article

VL - 36

SP - 71

EP - 75

JO - Pediatric Radiology

JF - Pediatric Radiology

SN - 0301-0449

IS - 1

ER -