Imaging manifestations of Niemann-Pick disease type B

William L. Simpson, David Mendelson, Melissa P. Wasserstein, Margaret M. McGovern

Research output: Contribution to journalReview article

14 Citations (Scopus)

Abstract

OBJECTIVE. The purpose of this article is to illustrate the various imaging manifestations of Niemann-Pick disease type B using various imaging techniques emphasizing crosssectional imaging. CONCLUSION. Niemann-Pick disease type B is a multisystem disease that affects the pulmonary, cardiovascular, abdominal, and skeletal systems. Cross-sectional imaging is well suited for detecting and assessing the various manifestations of this disease, which can be highly suggestive of the diagnosis when seen in combination.

Original languageEnglish (US)
JournalAmerican Journal of Roentgenology
Volume194
Issue number1
DOIs
StatePublished - Jan 2010
Externally publishedYes

Fingerprint

Type B Niemann-Pick Disease
Lung Diseases

Keywords

  • Hepatosplenomegaly
  • Lysosomal storage disease
  • Niemann-Pick disease
  • Pediatrics
  • Pulmonary

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging

Cite this

Imaging manifestations of Niemann-Pick disease type B. / Simpson, William L.; Mendelson, David; Wasserstein, Melissa P.; McGovern, Margaret M.

In: American Journal of Roentgenology, Vol. 194, No. 1, 01.2010.

Research output: Contribution to journalReview article

Simpson, William L. ; Mendelson, David ; Wasserstein, Melissa P. ; McGovern, Margaret M. / Imaging manifestations of Niemann-Pick disease type B. In: American Journal of Roentgenology. 2010 ; Vol. 194, No. 1.
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