Kinsfolk with dominant neurosensory hearing loss were studied in 4 generations. The temporal bones of one of the affected kinsmen were examined. These showed severe atrophy of the spiral ganglion cells in the lower two thirds of the cochlea, marked cystic changes in the spiral ligament, cystic changes in the stria vascularis, minimal loss of hair cells, and a focus of otosclerotic bone at the oval window.
|Original language||English (US)|
|Journal||Transactions of the American Academy of Ophthalmology and Otolaryngology|
|State||Published - Jan 1 1974|
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