Dominant neurosensory hearing loss: genetic, audiologic, and histopathologic correlates

Y. Rapoport, Robert J. Ruben

Research output: Chapter in Book/Report/Conference proceedingChapter

5 Citations (Scopus)

Abstract

Kinsfolk with dominant neurosensory hearing loss were studied in 4 generations. The temporal bones of one of the affected kinsmen were examined. These showed severe atrophy of the spiral ganglion cells in the lower two thirds of the cochlea, marked cystic changes in the spiral ligament, cystic changes in the stria vascularis, minimal loss of hair cells, and a focus of otosclerotic bone at the oval window.

Original languageEnglish (US)
Title of host publicationTransactions of the American Academy of Ophthalmology and Otolaryngology
Volume78
Edition6
StatePublished - 1974

Fingerprint

Hearing Loss
Spiral Ligament of Cochlea
Stria Vascularis
Spiral Ganglion
Temporal Bone
Cochlea
Alopecia
Atrophy
Bone and Bones

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Rapoport, Y., & Ruben, R. J. (1974). Dominant neurosensory hearing loss: genetic, audiologic, and histopathologic correlates. In Transactions of the American Academy of Ophthalmology and Otolaryngology (6 ed., Vol. 78)

Dominant neurosensory hearing loss : genetic, audiologic, and histopathologic correlates. / Rapoport, Y.; Ruben, Robert J.

Transactions of the American Academy of Ophthalmology and Otolaryngology. Vol. 78 6. ed. 1974.

Research output: Chapter in Book/Report/Conference proceedingChapter

Rapoport, Y & Ruben, RJ 1974, Dominant neurosensory hearing loss: genetic, audiologic, and histopathologic correlates. in Transactions of the American Academy of Ophthalmology and Otolaryngology. 6 edn, vol. 78.
Rapoport Y, Ruben RJ. Dominant neurosensory hearing loss: genetic, audiologic, and histopathologic correlates. In Transactions of the American Academy of Ophthalmology and Otolaryngology. 6 ed. Vol. 78. 1974
Rapoport, Y. ; Ruben, Robert J. / Dominant neurosensory hearing loss : genetic, audiologic, and histopathologic correlates. Transactions of the American Academy of Ophthalmology and Otolaryngology. Vol. 78 6. ed. 1974.
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