Dominant neurosensory hearing loss: genetic, audiologic, and histopathologic correlates

Y. Rapoport, R. J. Ruben

Research output: Contribution to journalArticle

5 Scopus citations

Abstract

Kinsfolk with dominant neurosensory hearing loss were studied in 4 generations. The temporal bones of one of the affected kinsmen were examined. These showed severe atrophy of the spiral ganglion cells in the lower two thirds of the cochlea, marked cystic changes in the spiral ligament, cystic changes in the stria vascularis, minimal loss of hair cells, and a focus of otosclerotic bone at the oval window.

Original languageEnglish (US)
Pages (from-to)ORL423-435
JournalTransactions of the American Academy of Ophthalmology and Otolaryngology
Volume78
Issue number6
StatePublished - Jan 1 1974

ASJC Scopus subject areas

  • Medicine(all)

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