TY - JOUR
T1 - Dominant neurosensory hearing loss
T2 - genetic, audiologic, and histopathologic correlates
AU - Rapoport, Y.
AU - Ruben, R. J.
PY - 1974
Y1 - 1974
N2 - Kinsfolk with dominant neurosensory hearing loss were studied in 4 generations. The temporal bones of one of the affected kinsmen were examined. These showed severe atrophy of the spiral ganglion cells in the lower two thirds of the cochlea, marked cystic changes in the spiral ligament, cystic changes in the stria vascularis, minimal loss of hair cells, and a focus of otosclerotic bone at the oval window.
AB - Kinsfolk with dominant neurosensory hearing loss were studied in 4 generations. The temporal bones of one of the affected kinsmen were examined. These showed severe atrophy of the spiral ganglion cells in the lower two thirds of the cochlea, marked cystic changes in the spiral ligament, cystic changes in the stria vascularis, minimal loss of hair cells, and a focus of otosclerotic bone at the oval window.
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M3 - Article
AN - SCOPUS:0016315370
SN - 0002-7154
VL - 78
SP - ORL423-435
JO - Transactions of the American Academy of Ophthalmology and Otolaryngology
JF - Transactions of the American Academy of Ophthalmology and Otolaryngology
IS - 6
ER -