Desmoplastic small round cell tumor: postoperative retroperitoneal mass

Colette J. Shen, David M. Loeb, Stephanie A. Terezakis

Research output: Contribution to journalArticle

Abstract

We describe the case of a 14-year-old boy who presented with a large, 17.6-cm retroperitoneal mass, along with multiple metastases, and was diagnosed with desmoplastic small round cell tumor. After initial chemotherapy, he underwent gross total resection with a positive margin. On postoperative radiation planning computed tomography, a 6.8-cm heterogeneous mass was noted in the surgical bed. Given the tumor's aggressive nature and positive surgical margins, there was real concern for recurrent disease. Further evaluation with magnetic resonance imaging elucidated that the mass consisted of simple fluid and fat, without contrast enhancement, suggesting a postoperative fluid collection. He was able to continue with adjuvant treatment as planned. This case example illustrates that even large postoperative heterogeneous masses may still be related to postoperative fluid collection in patients with aggressive tumor. However, it is important to rule out recurrent disease before starting adjuvant therapy given improved outcomes with gross total resection in desmoplastic small round cell tumor.

Original languageEnglish (US)
Pages (from-to)248-250
Number of pages3
JournalRadiology Case Reports
Volume11
Issue number3
DOIs
StatePublished - Sep 1 2016
Externally publishedYes

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Desmoplastic Small Round Cell Tumor
Neoplasms
Fats
Tomography
Magnetic Resonance Imaging
Radiation
Neoplasm Metastasis
Drug Therapy
Therapeutics

Keywords

  • Desmoplastic small round cell tumor
  • Postoperative

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging

Cite this

Desmoplastic small round cell tumor : postoperative retroperitoneal mass. / Shen, Colette J.; Loeb, David M.; Terezakis, Stephanie A.

In: Radiology Case Reports, Vol. 11, No. 3, 01.09.2016, p. 248-250.

Research output: Contribution to journalArticle

Shen, Colette J. ; Loeb, David M. ; Terezakis, Stephanie A. / Desmoplastic small round cell tumor : postoperative retroperitoneal mass. In: Radiology Case Reports. 2016 ; Vol. 11, No. 3. pp. 248-250.
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