Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child

Tulay Guran; Serap Turan; Behzat Ozkan; Su Gulsun Berrak; Cengiz Canpolat; Tolga Dagli; Funda Sirin Eren; Abdullah Bereket

doi:10.1515/JPEM.2009.22.4.363

Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child

Tulay Guran, Serap Turan, Behzat Ozkan, Su Gulsun Berrak, Cengiz Canpolat, Tolga Dagli, Funda Sirin Eren, Abdullah Bereket

Pediatrics

Research output: Contribution to journal › Article › peer-review

7 Scopus citations

Abstract

Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syn-drome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypo-kalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.

Original language	English (US)
Pages (from-to)	363-368
Number of pages	6
Journal	Journal of Pediatric Endocrinology and Metabolism
Volume	22
Issue number	4
DOIs	https://doi.org/10.1515/JPEM.2009.22.4.363
State	Published - Apr 2009

Keywords

Cushing's syndrome
Ectopic ACTH
Ewing's sarcoma
PNET

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Endocrinology, Diabetes and Metabolism
Endocrinology

UN SDGs

This output contributes to the following UN Sustainable Development Goals (SDGs)

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10.1515/JPEM.2009.22.4.363

Cite this

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title = "Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child",

abstract = "Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syn-drome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypo-kalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.",

keywords = "Cushing's syndrome, Ectopic ACTH, Ewing's sarcoma, PNET",

author = "Tulay Guran and Serap Turan and Behzat Ozkan and Berrak, {Su Gulsun} and Cengiz Canpolat and Tolga Dagli and Eren, {Funda Sirin} and Abdullah Bereket",

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T1 - Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child

AU - Guran, Tulay

AU - Turan, Serap

AU - Ozkan, Behzat

AU - Berrak, Su Gulsun

AU - Canpolat, Cengiz

AU - Dagli, Tolga

AU - Eren, Funda Sirin

AU - Bereket, Abdullah

PY - 2009/4

Y1 - 2009/4

N2 - Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syn-drome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypo-kalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.

AB - Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syn-drome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypo-kalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.

KW - Cushing's syndrome

KW - Ectopic ACTH

KW - Ewing's sarcoma

KW - PNET

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JO - Journal of Pediatric Endocrinology and Metabolism

JF - Journal of Pediatric Endocrinology and Metabolism

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ER -

Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child

Abstract

Keywords

ASJC Scopus subject areas

UN SDGs

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