Abstract
Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syn-drome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypo-kalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.
| Original language | English (US) |
|---|---|
| Pages (from-to) | 363-368 |
| Number of pages | 6 |
| Journal | Journal of Pediatric Endocrinology and Metabolism |
| Volume | 22 |
| Issue number | 4 |
| State | Published - Apr 2009 |
| Externally published | Yes |
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Keywords
- Cushing's syndrome
- Ectopic ACTH
- Ewing's sarcoma
- PNET
ASJC Scopus subject areas
- Endocrinology
- Endocrinology, Diabetes and Metabolism
- Pediatrics, Perinatology, and Child Health
Cite this
Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child. / Guran, Tulay; Turan, Serap; Ozkan, Behzat; Berrak, Su Gulsun; Canpolat, Cengiz; Dagli, Tolga; Eren, Funda Sirin; Bereket, Abdullah.
In: Journal of Pediatric Endocrinology and Metabolism, Vol. 22, No. 4, 04.2009, p. 363-368.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child
AU - Guran, Tulay
AU - Turan, Serap
AU - Ozkan, Behzat
AU - Berrak, Su Gulsun
AU - Canpolat, Cengiz
AU - Dagli, Tolga
AU - Eren, Funda Sirin
AU - Bereket, Abdullah
PY - 2009/4
Y1 - 2009/4
N2 - Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syn-drome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypo-kalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.
AB - Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syn-drome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypo-kalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.
KW - Cushing's syndrome
KW - Ectopic ACTH
KW - Ewing's sarcoma
KW - PNET
UR - http://www.scopus.com/inward/record.url?scp=67649306793&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=67649306793&partnerID=8YFLogxK
M3 - Article
C2 - 19554811
AN - SCOPUS:67649306793
VL - 22
SP - 363
EP - 368
JO - Journal of Pediatric Endocrinology and Metabolism
JF - Journal of Pediatric Endocrinology and Metabolism
SN - 0334-018X
IS - 4
ER -