Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child

Tulay Guran, Serap Turan, Behzat Ozkan, Su Gulsun Berrak, Cengiz Canpolat, Tolga Dagli, Funda Sirin Eren, Abdullah Bereket

Research output: Contribution to journalArticle

4 Citations (Scopus)

Abstract

Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syn-drome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypo-kalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.

Original languageEnglish (US)
Pages (from-to)363-368
Number of pages6
JournalJournal of Pediatric Endocrinology and Metabolism
Volume22
Issue number4
StatePublished - Apr 2009
Externally publishedYes

Fingerprint

Ectopic ACTH Syndrome
Ewing's Sarcoma
Cushing Syndrome
Adrenocorticotropic Hormone
Age Groups
Pediatrics
Growth
Neoplasms

Keywords

  • Cushing's syndrome
  • Ectopic ACTH
  • Ewing's sarcoma
  • PNET

ASJC Scopus subject areas

  • Endocrinology
  • Endocrinology, Diabetes and Metabolism
  • Pediatrics, Perinatology, and Child Health

Cite this

Guran, T., Turan, S., Ozkan, B., Berrak, S. G., Canpolat, C., Dagli, T., ... Bereket, A. (2009). Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child. Journal of Pediatric Endocrinology and Metabolism, 22(4), 363-368.

Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child. / Guran, Tulay; Turan, Serap; Ozkan, Behzat; Berrak, Su Gulsun; Canpolat, Cengiz; Dagli, Tolga; Eren, Funda Sirin; Bereket, Abdullah.

In: Journal of Pediatric Endocrinology and Metabolism, Vol. 22, No. 4, 04.2009, p. 363-368.

Research output: Contribution to journalArticle

Guran, T, Turan, S, Ozkan, B, Berrak, SG, Canpolat, C, Dagli, T, Eren, FS & Bereket, A 2009, 'Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child', Journal of Pediatric Endocrinology and Metabolism, vol. 22, no. 4, pp. 363-368.
Guran, Tulay ; Turan, Serap ; Ozkan, Behzat ; Berrak, Su Gulsun ; Canpolat, Cengiz ; Dagli, Tolga ; Eren, Funda Sirin ; Bereket, Abdullah. / Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child. In: Journal of Pediatric Endocrinology and Metabolism. 2009 ; Vol. 22, No. 4. pp. 363-368.
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