Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child

Tulay Guran; Serap Turan; Behzat Ozkan; Su Gulsun Berrak; Cengiz Canpolat; Tolga Dagli; Funda Sirin Eren; Abdullah Bereket

doi:10.1515/JPEM.2009.22.4.363

Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child

Tulay Guran, Serap Turan, Behzat Ozkan, Su Gulsun Berrak, Cengiz Canpolat, Tolga Dagli, Funda Sirin Eren, Abdullah Bereket

Pediatrics

Research output: Contribution to journal › Article › peer-review

7 Scopus citations

Abstract

Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syn-drome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypo-kalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.

Original language	English (US)
Pages (from-to)	363-368
Number of pages	6
Journal	Journal of Pediatric Endocrinology and Metabolism
Volume	22
Issue number	4
DOIs	https://doi.org/10.1515/JPEM.2009.22.4.363
State	Published - Apr 2009

Keywords

Cushing's syndrome
Ectopic ACTH
Ewing's sarcoma
PNET

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Endocrinology, Diabetes and Metabolism
Endocrinology

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10.1515/JPEM.2009.22.4.363

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title = "Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child",

abstract = "Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syn-drome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypo-kalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.",

keywords = "Cushing's syndrome, Ectopic ACTH, Ewing's sarcoma, PNET",

author = "Tulay Guran and Serap Turan and Behzat Ozkan and Berrak, {Su Gulsun} and Cengiz Canpolat and Tolga Dagli and Eren, {Funda Sirin} and Abdullah Bereket",

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T1 - Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child

AU - Guran, Tulay

AU - Turan, Serap

AU - Ozkan, Behzat

AU - Berrak, Su Gulsun

AU - Canpolat, Cengiz

AU - Dagli, Tolga

AU - Eren, Funda Sirin

AU - Bereket, Abdullah

PY - 2009/4

Y1 - 2009/4

N2 - Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syn-drome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypo-kalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.

AB - Ectopic ACTH syndrome (EAS) is extremely rare in the pediatric age group. Sarcomatous tumors causing EAS are even rarer. We report a 9 year-old girl presenting with Cushing's syn-drome caused by ectopic ACTH production by a Ewing's sarcoma. This case illustrates that rapid appearance of Cushingoid symptoms, absence of growth retardation and the presence of hypo-kalemia are suggestive clues for ectopic ACTH production as the source of Cushing's syndrome.

KW - Cushing's syndrome

KW - Ectopic ACTH

KW - Ewing's sarcoma

KW - PNET

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JO - Journal of Pediatric Endocrinology and Metabolism

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ER -

Cushing's syndrome due to a non-adrenal ectopic adrenocorticotropin- secreting ewing's sarcoma in a child

Abstract

Keywords

ASJC Scopus subject areas

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