Complete Atresia of Coronary Ostia in Pulmonary Atresia and Intact Ventricular Septum

S. E. Selamet, Daphne T. Hsu, H. M. Thaker, W. M. Gersony

Research output: Contribution to journalArticle

24 Citations (Scopus)

Abstract

We describe the clinical course, echocardiography, angiography, and histopathology of a female infant with pulmonary atresia and intact ventricular septum (PA/IVS) with complete coronary ostial atresia and right ventricle-dependent coronary circulation who survived for 7 weeks after palliative surgery. The patient expired from myocardial insufficiency while waiting for a donor heart. Postmortem examination demonstrated atretic coronary ostia, ventricular sinusoids, and myocardial infarctions of various ages. This report suggests that neonates with PA/IVS who have this extreme form of coronary abnormality may potentially be managed medically and surgically until cardiac transplantation is available.

Original languageEnglish (US)
Pages (from-to)67-69
Number of pages3
JournalPediatric Cardiology
Volume25
Issue number1
DOIs
StatePublished - Jan 2004
Externally publishedYes

Fingerprint

Pulmonary Atresia
Ventricular Septum
Coronary Circulation
Heart Transplantation
Palliative Care
Heart Ventricles
Echocardiography
Autopsy
Angiography
Myocardial Infarction
Tissue Donors
Newborn Infant
Pulmonary Atresia with Intact Ventricular Septum

Keywords

  • Atresia of Coronary Ostia
  • Ischemia
  • Myocardial Infarction
  • Pulmonary Atresia

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Pediatrics, Perinatology, and Child Health

Cite this

Complete Atresia of Coronary Ostia in Pulmonary Atresia and Intact Ventricular Septum. / Selamet, S. E.; Hsu, Daphne T.; Thaker, H. M.; Gersony, W. M.

In: Pediatric Cardiology, Vol. 25, No. 1, 01.2004, p. 67-69.

Research output: Contribution to journalArticle

Selamet, S. E. ; Hsu, Daphne T. ; Thaker, H. M. ; Gersony, W. M. / Complete Atresia of Coronary Ostia in Pulmonary Atresia and Intact Ventricular Septum. In: Pediatric Cardiology. 2004 ; Vol. 25, No. 1. pp. 67-69.
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