Complete Atresia of Coronary Ostia in Pulmonary Atresia and Intact Ventricular Septum

S. E. Selamet; D. T. Hsu; H. M. Thaker; W. M. Gersony

doi:10.1007/s00246-003-0517-0

Complete Atresia of Coronary Ostia in Pulmonary Atresia and Intact Ventricular Septum

S. E. Selamet, D. T. Hsu, H. M. Thaker, W. M. Gersony

Research output: Contribution to journal › Article › peer-review

26 Scopus citations

Abstract

We describe the clinical course, echocardiography, angiography, and histopathology of a female infant with pulmonary atresia and intact ventricular septum (PA/IVS) with complete coronary ostial atresia and right ventricle-dependent coronary circulation who survived for 7 weeks after palliative surgery. The patient expired from myocardial insufficiency while waiting for a donor heart. Postmortem examination demonstrated atretic coronary ostia, ventricular sinusoids, and myocardial infarctions of various ages. This report suggests that neonates with PA/IVS who have this extreme form of coronary abnormality may potentially be managed medically and surgically until cardiac transplantation is available.

Original language	English (US)
Pages (from-to)	67-69
Number of pages	3
Journal	Pediatric Cardiology
Volume	25
Issue number	1
DOIs	https://doi.org/10.1007/s00246-003-0517-0
State	Published - Jan 2004
Externally published	Yes

Keywords

Atresia of Coronary Ostia
Ischemia
Myocardial Infarction
Pulmonary Atresia

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Cardiology and Cardiovascular Medicine

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10.1007/s00246-003-0517-0

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abstract = "We describe the clinical course, echocardiography, angiography, and histopathology of a female infant with pulmonary atresia and intact ventricular septum (PA/IVS) with complete coronary ostial atresia and right ventricle-dependent coronary circulation who survived for 7 weeks after palliative surgery. The patient expired from myocardial insufficiency while waiting for a donor heart. Postmortem examination demonstrated atretic coronary ostia, ventricular sinusoids, and myocardial infarctions of various ages. This report suggests that neonates with PA/IVS who have this extreme form of coronary abnormality may potentially be managed medically and surgically until cardiac transplantation is available.",

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AU - Selamet, S. E.

AU - Hsu, D. T.

AU - Thaker, H. M.

AU - Gersony, W. M.

PY - 2004/1

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N2 - We describe the clinical course, echocardiography, angiography, and histopathology of a female infant with pulmonary atresia and intact ventricular septum (PA/IVS) with complete coronary ostial atresia and right ventricle-dependent coronary circulation who survived for 7 weeks after palliative surgery. The patient expired from myocardial insufficiency while waiting for a donor heart. Postmortem examination demonstrated atretic coronary ostia, ventricular sinusoids, and myocardial infarctions of various ages. This report suggests that neonates with PA/IVS who have this extreme form of coronary abnormality may potentially be managed medically and surgically until cardiac transplantation is available.

AB - We describe the clinical course, echocardiography, angiography, and histopathology of a female infant with pulmonary atresia and intact ventricular septum (PA/IVS) with complete coronary ostial atresia and right ventricle-dependent coronary circulation who survived for 7 weeks after palliative surgery. The patient expired from myocardial insufficiency while waiting for a donor heart. Postmortem examination demonstrated atretic coronary ostia, ventricular sinusoids, and myocardial infarctions of various ages. This report suggests that neonates with PA/IVS who have this extreme form of coronary abnormality may potentially be managed medically and surgically until cardiac transplantation is available.

KW - Atresia of Coronary Ostia

KW - Ischemia

KW - Myocardial Infarction

KW - Pulmonary Atresia

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Complete Atresia of Coronary Ostia in Pulmonary Atresia and Intact Ventricular Septum

Abstract

Keywords

ASJC Scopus subject areas

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