Complete Atresia of Coronary Ostia in Pulmonary Atresia and Intact Ventricular Septum

S. E. Selamet, D. T. Hsu, H. M. Thaker, W. M. Gersony

Research output: Contribution to journalArticle

24 Scopus citations

Abstract

We describe the clinical course, echocardiography, angiography, and histopathology of a female infant with pulmonary atresia and intact ventricular septum (PA/IVS) with complete coronary ostial atresia and right ventricle-dependent coronary circulation who survived for 7 weeks after palliative surgery. The patient expired from myocardial insufficiency while waiting for a donor heart. Postmortem examination demonstrated atretic coronary ostia, ventricular sinusoids, and myocardial infarctions of various ages. This report suggests that neonates with PA/IVS who have this extreme form of coronary abnormality may potentially be managed medically and surgically until cardiac transplantation is available.

Original languageEnglish (US)
Pages (from-to)67-69
Number of pages3
JournalPediatric Cardiology
Volume25
Issue number1
DOIs
Publication statusPublished - Jan 1 2004
Externally publishedYes

    Fingerprint

Keywords

  • Atresia of Coronary Ostia
  • Ischemia
  • Myocardial Infarction
  • Pulmonary Atresia

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Cardiology and Cardiovascular Medicine

Cite this