Candida Retinitis in Bare Lymphocyte Syndrome

Jeremy Chess; Sherry Kaplan; Arye Rubinstein; Frederick Wang; Andrew Wiznia

doi:10.1016/S0161-6420(86)33683-2

Candida Retinitis in Bare Lymphocyte Syndrome

Jeremy Chess, Sherry Kaplan, Arye Rubinstein, Frederick Wang, Andrew Wiznia

Pediatrics

Research output: Contribution to journal › Article › peer-review

3 Scopus citations

Abstract

Bare lymphocyte syndrome (BLS) is a rare, severe combined immunodeficiency characterized by lack of expression of HLA A, Band C antigens and the absence of B₂ microglobulins. Patients with BlS exhibit functional deficiency of both T and B cells resulting in bacterial as well as viral and fungal infection. Ophthalmic findings in this group of disorders have not been reported. We present a case of candida retinitis in a terminally ill 5-year-old girl with BLS.

Original language	English (US)
Pages (from-to)	696-698
Number of pages	3
Journal	Ophthalmology
Volume	93
Issue number	5
DOIs	https://doi.org/10.1016/S0161-6420(86)33683-2
State	Published - 1986

Keywords

amphotericin B
bare lymphocyte syndrome
candida retinitis
combined immunodeficiency syndrome

ASJC Scopus subject areas

Ophthalmology

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10.1016/S0161-6420(86)33683-2

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title = "Candida Retinitis in Bare Lymphocyte Syndrome",

abstract = "Bare lymphocyte syndrome (BLS) is a rare, severe combined immunodeficiency characterized by lack of expression of HLA A, Band C antigens and the absence of B2 microglobulins. Patients with BlS exhibit functional deficiency of both T and B cells resulting in bacterial as well as viral and fungal infection. Ophthalmic findings in this group of disorders have not been reported. We present a case of candida retinitis in a terminally ill 5-year-old girl with BLS.",

keywords = "amphotericin B, bare lymphocyte syndrome, candida retinitis, combined immunodeficiency syndrome",

author = "Jeremy Chess and Sherry Kaplan and Arye Rubinstein and Frederick Wang and Andrew Wiznia",

year = "1986",

doi = "10.1016/S0161-6420(86)33683-2",

language = "English (US)",

volume = "93",

pages = "696--698",

journal = "Ophthalmology",

issn = "0161-6420",

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TY - JOUR

T1 - Candida Retinitis in Bare Lymphocyte Syndrome

AU - Chess, Jeremy

AU - Kaplan, Sherry

AU - Rubinstein, Arye

AU - Wang, Frederick

AU - Wiznia, Andrew

PY - 1986

Y1 - 1986

N2 - Bare lymphocyte syndrome (BLS) is a rare, severe combined immunodeficiency characterized by lack of expression of HLA A, Band C antigens and the absence of B2 microglobulins. Patients with BlS exhibit functional deficiency of both T and B cells resulting in bacterial as well as viral and fungal infection. Ophthalmic findings in this group of disorders have not been reported. We present a case of candida retinitis in a terminally ill 5-year-old girl with BLS.

AB - Bare lymphocyte syndrome (BLS) is a rare, severe combined immunodeficiency characterized by lack of expression of HLA A, Band C antigens and the absence of B2 microglobulins. Patients with BlS exhibit functional deficiency of both T and B cells resulting in bacterial as well as viral and fungal infection. Ophthalmic findings in this group of disorders have not been reported. We present a case of candida retinitis in a terminally ill 5-year-old girl with BLS.

KW - amphotericin B

KW - bare lymphocyte syndrome

KW - candida retinitis

KW - combined immunodeficiency syndrome

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U2 - 10.1016/S0161-6420(86)33683-2

DO - 10.1016/S0161-6420(86)33683-2

M3 - Article

C2 - 3725326

AN - SCOPUS:0022534771

SN - 0161-6420

VL - 93

SP - 696

EP - 698

JO - Ophthalmology

JF - Ophthalmology

IS - 5

ER -

Candida Retinitis in Bare Lymphocyte Syndrome

Abstract

Keywords

ASJC Scopus subject areas

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