A Rare Case of Large Epididymal Cyst in Androgen Insensitivity Syndrome Removed Laparoscopically

Alka Kriplani, S. Savithrisowmya, Nutan Agarwal, Pradeep Garg, Deepa Maheswari, A. C. Ammini, K. D Anand Rajan

Research output: Contribution to journalArticle

3 Citations (Scopus)

Abstract

Androgen insensitivity syndrome is a disorder of sexual differentiation with 46XY karyotype. The gonad is at risk (33% by 50 years of age) for development of malignant tumors. Hence, gonadectomy is warranted. We present a case of a 22-year-old woman diagnosed with androgen insensitivity syndrome during investigation of primary amenorrhea. Ultrasonography showed intraabdominally-located gonads, with a large, nontender cyst of 9.2 × 5.6 × 5.4 cm size, with limited mobility, to the right of the midline. There was also a partial septum, with a wall thickness of 1 to 2 mm and containing clear fluid. Because of suspicion of malignancy, complete surgery including laparoscopic peritoneal cytologic study, gonadectomy, lymphadenectomy, and omentectomy were performed. Histopathologic study showed testis with an epididymal cyst. Formation of epididymal cyst is rare in these cases. The patient did well in the postoperative period. She was put on hormone replacement therapy and is doing well.

Original languageEnglish (US)
Pages (from-to)504-506
Number of pages3
JournalJournal of Minimally Invasive Gynecology
Volume16
Issue number4
DOIs
StatePublished - Jul 2009
Externally publishedYes

Fingerprint

Spermatocele
Androgen-Insensitivity Syndrome
Gonads
Disorders of Sex Development
Amenorrhea
Hormone Replacement Therapy
Lymph Node Excision
Karyotype
Postoperative Period
Laparoscopy
Testis
Cysts
Ultrasonography
Neoplasms

Keywords

  • Androgen insensitivity syndrome
  • Epididymal cyst
  • Gonadectomy
  • Laparoscopy
  • Testicular feminization syndrome

ASJC Scopus subject areas

  • Obstetrics and Gynecology

Cite this

Kriplani, A., Savithrisowmya, S., Agarwal, N., Garg, P., Maheswari, D., Ammini, A. C., & Rajan, K. D. A. (2009). A Rare Case of Large Epididymal Cyst in Androgen Insensitivity Syndrome Removed Laparoscopically. Journal of Minimally Invasive Gynecology, 16(4), 504-506. https://doi.org/10.1016/j.jmig.2009.04.013

A Rare Case of Large Epididymal Cyst in Androgen Insensitivity Syndrome Removed Laparoscopically. / Kriplani, Alka; Savithrisowmya, S.; Agarwal, Nutan; Garg, Pradeep; Maheswari, Deepa; Ammini, A. C.; Rajan, K. D Anand.

In: Journal of Minimally Invasive Gynecology, Vol. 16, No. 4, 07.2009, p. 504-506.

Research output: Contribution to journalArticle

Kriplani, A, Savithrisowmya, S, Agarwal, N, Garg, P, Maheswari, D, Ammini, AC & Rajan, KDA 2009, 'A Rare Case of Large Epididymal Cyst in Androgen Insensitivity Syndrome Removed Laparoscopically', Journal of Minimally Invasive Gynecology, vol. 16, no. 4, pp. 504-506. https://doi.org/10.1016/j.jmig.2009.04.013
Kriplani, Alka ; Savithrisowmya, S. ; Agarwal, Nutan ; Garg, Pradeep ; Maheswari, Deepa ; Ammini, A. C. ; Rajan, K. D Anand. / A Rare Case of Large Epididymal Cyst in Androgen Insensitivity Syndrome Removed Laparoscopically. In: Journal of Minimally Invasive Gynecology. 2009 ; Vol. 16, No. 4. pp. 504-506.
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