A rare case of isolated congenital right ventricular inflow obstruction: Due to the presence of an intraventricular muscular shelf

Giovanni J. Nanna, Michael G. Nanna, Danielle Muchnik, Joseph J. DeRose, Seshasayee Narasimhan

Research output: Contribution to journalArticle

Abstract

A 56-year-old man presented with anasarca and a 40-lb weight gain that had occurred over the course of 3 to 4 weeks. He had a history of permanent atrial fibrillation and a congenital anomaly of the right ventricular inflow tract. This defect consisted of a muscular shelf in the right ventricular inflow tract, which encased the tricuspid subvalvular apparatus in such a manner that it created tricuspid stenosis. The clinical consequences of this anatomic and hemodynamic situation were a massively dilated right atrium, permanent atrial fibrillation, and clinical evidence of right-sided heart failure, including fluid retention and ascites. The patient underwent surgical resection of the muscular shelf, which was followed by progressive resolution of the ascites and fluid retention.

Original languageEnglish (US)
Pages (from-to)557-559
Number of pages3
JournalTexas Heart Institute Journal
Volume39
Issue number4
StatePublished - Aug 1 2012

Keywords

  • Anasarca
  • Heart defects, congenital/etiology
  • Hidadenitis
  • Right ventricular obstruction
  • Tricuspid valve stenosis/congenital/ therapy
  • Tricuspid valve/ pathology

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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