A challenging case of hepatoblastoma concomitant with autosomal recessive polycystic kidney disease and Caroli syndrome-Review of the literature

Nevil Kadakia, Steven J. Lobritto, Nadia Ovchinsky, Helen E. Remotti, Darrell J. Yamashiro, Jean C. Emond, Mercedes Martinez

Research output: Contribution to journalArticle

1 Citation (Scopus)

Abstract

We report a rare case of an 18-month-old female with autosomal recessive polycystic kidney disease, Caroli syndrome, and pure fetal type hepatoblastoma. The liver tumor was surgically resected with no chemotherapy given. Now 9 years post resection she demonstrates no local or distant recurrence and stable renal function.

Original languageEnglish (US)
Article number114
JournalFrontiers in Pediatrics
Volume5
DOIs
StatePublished - Jun 7 2017

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Autosomal Recessive Polycystic Kidney
Caroli Disease
Hepatoblastoma
Kidney
Recurrence
Drug Therapy
Liver
Neoplasms

Keywords

  • Autosomal recessive polycystic kidney disease
  • Caroli syndrome
  • Congenital hepatic fibrosis
  • Hepatoblastoma
  • Hepatorenal fibrocystic diseases

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

Cite this

A challenging case of hepatoblastoma concomitant with autosomal recessive polycystic kidney disease and Caroli syndrome-Review of the literature. / Kadakia, Nevil; Lobritto, Steven J.; Ovchinsky, Nadia; Remotti, Helen E.; Yamashiro, Darrell J.; Emond, Jean C.; Martinez, Mercedes.

In: Frontiers in Pediatrics, Vol. 5, 114, 07.06.2017.

Research output: Contribution to journalArticle

Kadakia, Nevil ; Lobritto, Steven J. ; Ovchinsky, Nadia ; Remotti, Helen E. ; Yamashiro, Darrell J. ; Emond, Jean C. ; Martinez, Mercedes. / A challenging case of hepatoblastoma concomitant with autosomal recessive polycystic kidney disease and Caroli syndrome-Review of the literature. In: Frontiers in Pediatrics. 2017 ; Vol. 5.
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