A challenging case of hepatoblastoma concomitant with autosomal recessive polycystic kidney disease and Caroli syndrome-Review of the literature

Nevil Kadakia, Steven J. Lobritto, Nadia Ovchinsky, Helen E. Remotti, Darrell J. Yamashiro, Jean C. Emond, Mercedes Martinez

Research output: Contribution to journalArticle

2 Scopus citations

Abstract

We report a rare case of an 18-month-old female with autosomal recessive polycystic kidney disease, Caroli syndrome, and pure fetal type hepatoblastoma. The liver tumor was surgically resected with no chemotherapy given. Now 9 years post resection she demonstrates no local or distant recurrence and stable renal function.

Original languageEnglish (US)
Article number114
JournalFrontiers in Pediatrics
Volume5
DOIs
StatePublished - Jun 7 2017

Keywords

  • Autosomal recessive polycystic kidney disease
  • Caroli syndrome
  • Congenital hepatic fibrosis
  • Hepatoblastoma
  • Hepatorenal fibrocystic diseases

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

Fingerprint Dive into the research topics of 'A challenging case of hepatoblastoma concomitant with autosomal recessive polycystic kidney disease and Caroli syndrome-Review of the literature'. Together they form a unique fingerprint.

  • Cite this